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肺动脉高压诊治中值得注意的几个问题
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- Author:
- No author available
- Journal Title:
- National Medical Journal of China
- Issue:
- 40
- DOI:
- 10.3760/cma.j.issn.0376-2491.2013.40.002
- Key Word:
- No keyword available
Abstract： 近10年来我国肺动脉高压的研究蓬勃发展,取得了长足进展.临床医师对肺动脉高压的诊治水平有所提高,令人欣慰,但在对肺动脉高压的认识及诊治中仍存在不少问题或误区.现就其中一些主要问题阐述如下,希冀同行们批评指正.一、肺动脉高压是罕见病吗?首先,各国对罕见病的定义各不相同,而世界卫生组织则将发病人数小于总人口的6.5/万～10.0/万的疾病定义为罕见病[1].目前,我国官方尚未确定罕见病的定义.有学者建议将我国发病率＜1/万(指新生儿)或患病率＜1/50万的疾病列为罕见病.
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