Pituitary stalk interruption syndrome in newborn: a case report
- Author:
- No author available
- Journal Title:
- Chinese Journal of Perinatal Medicine
- Issue:
- 12
- DOI:
- 10.3760/cma.j.issn.1007-9408.2019.12.010
- Key Word:
- 垂体疾病;低血糖症;甲状腺功能减退症;婴儿,新生;Pituitary diseases;Hypoglycemia;Hypothyroidism;Infant,newborn
Abstract： This study reported a postterm female infant born at 43+2 weeks of gestation via cesarean section with a birth weight of 2 950 g.Cyanosis was presented around 14 h after birth.Laboratory test results showed that the blood glucose was 1.4 mmol/L and the levels of free triiodothyronine (FT3),free tetraiodothyronine (FT4),thyrotropin (TSH),growth hormone (GH) and insulin-like growth factor-1 (IGF-1) were significantly reduced.Cranial MRI confirmed the diagnosis of pituitary stalk interruption syndrome.The baby girl was treated with hydrocortisone and levothyroxine and discharged following clinical symptoms improvement and blood glucose normalization.Follow-up data showed unstable blood glucose and hypothyroidism at six and 10 months after birth and growth retardation at 15 months.
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