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Etiology of childhood bronchiectasis: strategy of early diagnosis and management

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Author:
No author available
Journal Title:
CHINESE JOURNAL OF PEDIATRICS
Issue:
2
DOI:
10.3760/cma.j.issn.0578-1310.2011.02.010
Key Word:
No keyword available

Abstract: @@ 囊性纤维化(Cystic fibrosis,CF)是一种常染色体隐性遗传性疾病,它是引起白种人儿童支气管扩张(bronchiectasis)的主要原因.而非囊性纤维化支气管扩张(non-cystic fibrosis bronchiectasis)常见于发展中国家,以前认为它主要见于慢性化脓性炎症,表现为支气管不可逆的扩张伴有管壁增厚及破坏.随着高分辨率CT(HRCT)技术的发展,结合近年来大量的研究结果显示,非囊性纤维化支气管扩张在发达国家的诊断率也不断增多.

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