You Position: Home > Paper
特发性胸膜肺弹力纤维增生症一例
( views:98, downloads:795 )
- Author:
- No author available
- Journal Title:
- Chinese Journal of Tuberculosis and Respiratory Diseases
- Issue:
- 8
- DOI:
- 10.3760/cma.j.issn.1001-0939.2014.08.017
- Key Word:
- No keyword available
Abstract： 特发性胸膜肺弹力纤维增生症(pleuroparenchymal fibroelastosis,PPFE)是一种罕见的新型特发性间质性肺炎(idiopathic interstitial pneumonia,IIP)[1],国际上也仅有一些散在的病例报道,国内尚无此类病例.现将我院新近确诊的一例PPFE病例报道如下,以提高对该病的认识.患者男,34岁,因“肺部阴影10余年,咳嗽、活动后气短4年”于2013年11月入院.患者于2003年体检时发现肺部阴影,胸部CT示“双上肺为主的纤维索条影”,因无明显临床症状,未进一步诊治.2009年10月患者受凉后出现发热、咳嗽,最高体温达38.1℃,无咳痰、咯血;伴有剧烈活动后气短,复查胸部CT示“双上肺胸膜下为主的斑片状和条索状影,局限性胸膜增厚”,考虑“弥漫性肺病变性质不明”,给予抗感染治疗后体温下降,咳嗽症状有所缓解,但仍有咳嗽、气短,并在感冒后加重.自2013年3月再次感冒后出现咳嗽、活动后气短加重,平地步行500 m左右、步行上3层楼等活动即有气短.
- [1]冯瑞娥.一种新的特发性间质性肺炎类型：特发性胸膜间质弹力纤维化[J].2013,(5).
- [2]Watanabe,K..Pleuroparenchymal fibroelastosis: Its clinical characteristics[J].2013,9(4).
- [3]Hideki, Kusagaya,Yutaro, Nakamura,Masato, Kono,etc.Idiopathic pleuroparenchymal fibroelastosis: consideration of a clinicopathological entity in a series of Japanese patients.[J].2012,12.
- [4]Sara Piciucchi,Sara Tomassetti,Gianluca Casoni,etc.High resolution CT and histological findings in idiopathic pleuroparenchymal fibroelastosis: Features and differential diagnosis[J].2011,12(1).
- [5]Gonzalo Labarca,Hernán Cabello,Sebastián Fernández Bussy,etc.A Case of Interstitial Lung Disease With Apical Pleural Thickening: Idiopathic Pleuroparenchymal Fibroelastosis[J].2014,50(1).
- [6]Stephen K, Frankel,Carlyne D, Cool,David A, Lynch,etc.Idiopathic pleuroparenchymal fibroelastosis: description of a novel clinicopathologic entity.[J].2004,126(6).
- [7]Andrew G. Nicholson,Elisabetta A. Renzoni,Suzy Guy,etc.Pleuroparenchymal fibroelastosis: a spectrum of histopathological and imaging phenotypes[J].2012,40(2).
- [8]William D, Travis,Ulrich, Costabel,David M, Hansell,etc.An official American Thoracic Society/European Respiratory Society statement: Update of the international multidisciplinary classification of the idiopathic interstitial pneumonias.[J].2013,188.
- [9]Kentaro, Watanabe,Nobuhiko, Nagata,Yasuhiko, Kitasato,etc.Rapid decrease in forced vital capacity in patients with idiopathic pulmonary upper lobe fibrosis.[J].2012,50(3).