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伴有环状小管的性索肿瘤一例
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- Author:
- No author available
- Journal Title:
- Chinese Journal of Obstetrics and Gynecology
- Issue:
- 9
- DOI:
- 10.3760/cma.j.issn.0529-567x.2019.09.012
- Key Word:
- No keyword available
Abstract： 伴有环状小管的性索肿瘤(SCTAT)是1种罕见的卵巢性索?间质肿瘤.SCTAT具有不同的临床表现,取决于是否伴有Petuz?Jeghers综合征(PJS).伴有PJS的SCTAT常累及双侧卵巢,多灶,生物学行为良性;不伴有PJS的SCTAT常为单侧,单灶,20%患者可出现恶性的临床经过.SCTAT的治疗多以保留生育功能手术为主.本文报道1例不伴有PJS的SCTAT.患者29岁,因"不孕2年,体检发现下腹部包块2个月"收入院,入院后行腹腔镜下左侧附件切除+右侧卵巢活检术,术后病理检查确诊为SCTAT.患者的口腔黏膜、唇和皮肤未见黑色素沉着,术后行胃肠镜检查未发现息肉,即不伴有PJS;术后患者恢复良好,未行放化疗.现结合文献复习对本病的临床特点、诊断、治疗及预后进行探讨.
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