You Position: Home > Paper

Cronkhite-Canada syndrome: A rare polyposis

( views:167, downloads:0 )
Author:
No author available
Journal Title:
World Chinese Journal of Digestology
Issue:
16
DOI:
10.11569/wcjd.v27.i16.977
Key Word:
Cronkhite-Canada综合征;自身免疫;IgG4;幽门螺杆菌;肠道菌群

Abstract: Cronkhite-Canada综合征(Cronkhite-Canada syndrome,CCS)是一组以胃肠道弥漫性息肉、指(趾)甲营养不良、脱发、皮肤色素沉着、腹泻、体重减轻和味觉障碍等为表现的非遗传性罕见病.多数CCS临床预后不良,常合并危及生命的严重并发症.目前关于CCS疾病的病因、发病机制及合理的治疗方案仍处于探索阶段.本文通过综述CCS目前常见病因、临床表现、内镜特点以及治疗方案,旨在提高临床工作中对CC S认识水平的同时并探索其病因及最佳的治疗策略.

WanfangData CO.,Ltd All Rights Reserved
About WanfangData | Contact US
Healthcare Department, Fuxing Road NO.15, Haidian District Beijing, 100038 P.R.China
Tel:+86-010-58882616 Fax:+86-010-58882615 Email:yiyao@wanfangdata.com.cn