Abstract： Choledochal cyst is one of the most common congenital diseases in the biliary tract system,which can affect both children and adults. While surgical management has changed markedly in recent years, researchers′ understanding related to the nomenclature,diagnosis and classification of choledochal cysts remains inadequate. Anatomical variations and stricture of the intrahepatic bile duct are prone to be overlooked during surgery. Furthermore, it is still controversial in the treatment of intrapancreatic choledochal cyst and the extent of resection related to dilated bile ducts. Along with the advancement of laparoscopic or robotic-assisted procedures,there is also an increase in reoperations for patients with choledochal cyst,which underscores the importance of long-term biliary patency. This state-of-the-art review on choledochal cyst aims to further improve the diagnosis and treatment of this benign but intractable disease.