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表现为支气管扩张的显微镜下多血管炎一例——疑点分析

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Author:
No author available
Journal Title:
Chinese Journal of Tuberculosis and Respiratory Diseases
Issue:
4
DOI:
10.3760/cma.j.issn.1001-0939.2019.04.020
Key Word:
No keyword available

Abstract: ANCA相关性血管炎(AAV)是一类以ANCA或抗MPO抗体或抗PR3抗体阳新为实验室特征的疾病,主要包括显微镜下多血管炎(MPA)和肉芽肿性多血管炎(GPA),嗜酸性肉芽肿性多血管炎(EGPA).文中患者虽有P-ANCA和抗MPO抗体阳性,有MPA一般临床特征,然而结合患者病史发展,实验室检查和影像学特点,均可能提示我们该患者在疾病演变,病情进展和最终诊断有很多值得商榷的疑点.

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