Paper - WANFANG MED ONLINE

You Position: Home > Paper

肺淋巴管平滑肌瘤病肺移植治疗研究进展

( views:299, downloads:258 )

Author:: No author available

Journal Title:: Chinese Journal of Tuberculosis and Respiratory Diseases

Issue:: 10

DOI:: 10.3760/cma.j.issn.1001-0939.2011.10.015

Key Word:: No keyword available

Abstract：肺淋巴管平滑肌瘤病(pulmonary lymphangioleiomyomatosis,PLAM)是一种罕见的、发病机制尚不清楚的弥漫性肺部疾病,常见于育龄期妇女,与结节性硬化症(tuberous sclerosis,TSC)基因1和2的突变有关[1,3].该病以异常的平滑肌细胞(LAM细胞)在气道、淋巴管及血管等中异常增殖为特点,最终导致肺实质形成薄壁囊状结构,肺功能减退甚至呼吸衰竭,从而危及患者生命.内科治疗效果欠佳,肺移植为目前惟一可能有效的治疗手段.

Reference

[1]Annette Boehler.Lung Transplantation for Cystic Lung Diseases: Lymphangioleiomyomatosis, Histiocytosis X, and Sarcoidosis[J].2001,22(5).
[2]Jay H, Ryu,Clint H, Doerr,Susan D, Fisher,etc.Chylothorax in lymphangioleiomyomatosis.[J].2003,123(2).
[3]J S, Nine,S A, Yousem,I L, Paradis,etc.Lymphangioleiomyomatosis: recurrence after lung transplantation.[J].1900,13.
[4]Muller NL,Kazerooni EA,McAdams HP,etc.Lung transplantation for lymphangioleiomyomatosis: role of imaging in the assessment of complications related to the underlying disease.[J].1999,210(2).
[5]Elpidio Calvo,Luis Amarillas,Miguel A. Mateos,etc.Lymphangioleiomyomatosis, chylous ascites, and diet[J].1996,41(3).
[6]F, Wellens,M, Estenne,P, de Francquen,etc.Combined heart-lung transplantation for terminal pulmonary lymphangioleiomyomatosis.[J].1985,89.
[7]K, Moriya,Y, Shinno,K, Kawakura,etc.[The natural history of renal angiomyolipoma].[J].1999,90(5).
[8]Kitaichi M,Nishimura K,Itoh H,etc.Pulmonary lymphangioleiomyomatosis: a report of 46 patients including a clinicopathologic study of prognostic factors.[J].1995.
[9]Shan C. Chu,Koji Horiba,Jiro Usuki,etc.Comprehensive Evaluation of 35 Patients With Lymphangioleiomyomatosis[J].1999,115(4).
[10]Avila Nilo A.,Dwyer Andrew J.,Rabel Antoinette,etc.CT of Pleural Abnormalities in Lymphangioleiomyomatosis and Comparison of Pleural Findings After Different Types of Pleurodesis[J].2006.
[11]Cordier JF,Lazor,Johnson SR.European Respiratory Society guidelines for the diagnosis and management of lymphangioleiomyomatosis.[J].2010,35(1).
[12]Evans A,Kpodonu J,Caines A,etc.The US Experience with Lung Transplantation for Pulmonary Lymphangioleiomyomatosis.[J].2005,24(9).
[13]Taylor, J.R.,Ryu, J..Lymphangioleiomyomatosis.[J].1990,323(18).
[14]Raghu G,Mulligan M,Billings ME.Acute constrictive pericarditis after lung transplantation for lymphangioleiomyomatosis.[J].2009,28(1).
[15]Iversen M,Milman N,Carlsen J,etc.Long-term survival after lung transplantation depends on development and severity of bronchiolitis obliterans syndrome.[J].2007,26(7).
[16]Johnson SR,Tattersfield AE.Clinical experience of lymphangioleiomyomatosis in the UK.[J].2000,55(12).
[17]J G, van Baal,N J, Smits,J N, Keeman,etc.The evolution of renal angiomyolipomas in patients with tuberous sclerosis.[J].1994,152.
[18]Trulock EP,Battafarano RJ,Cooper JD,etc.Lung transplantation for lymphangioleiomyomatosis.[J].2004,23(3).
[19]Treilhaud M,Grenet D,Stern M,etc.Lung transplantation for lymphangioleiomyomatosis: the French experience.[J].2008,86(4).
[20]Nakagawa T,Takeda K,Kobayashi S,etc.Renal angiomyolipoma: relationships between tumor size, aneurysm formation, and rupture.[J].2002,225(1).
[21]Boehler, Annette,Speich, Rudolf,Russi, Erich W.,etc.Lung Transplantation for Lymphangioleiomyomatosis.[J].1996,335(17).
[22]Speich R,Behr J,Boehler A,etc.Lung transplantation for lymphangioleiomyomatosis: the European experience.[J].2009,28(1).