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Isolated pulmonary giant cell arteritis:a case report and literature review

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Author:
No author available
Journal Title:
CHINESE JOURNAL OF TUBERCULOSIS AND RESPIRATORY DISEASES
Issue:
2
DOI:
10.3760/j:issn:1001-0939.2004.02.012
Key Word:
动脉炎;肺;巨细胞;文献复习

Abstract: 目的了解孤立性巨细胞性肺动脉炎的临床及病理表现.方法 1例右肺动脉完全堵塞患者,行右肺切除,标本取材后,石蜡包埋制片,苏木精-伊红及免疫组化染色.结合有关文献及本例患者的临床资料,对本病的临床及病理表现进行论述.结果本病的病理表现主要为肺动脉管壁增厚、纤维组织及小血管增生,淋巴细胞(主要为T淋巴细胞)、浆细胞、组织细胞及少量多核巨细胞浸润,管腔血栓形成及机化,肺出血性梗死.结论孤立性巨细胞性肺动脉炎是一种非常罕见的疾病,结合血管造影和病理检查可以确诊.

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