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Primary malignant peripheral nerve sheath tumor of the breast: a case report

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Author:
No author available
Journal Title:
Chinese Journal of Radiology
Issue:
2
DOI:
10.3760/cma.j.cn112149-20200611-00804
Key Word:
乳腺肿瘤;磁共振成像;恶性周围神经鞘膜瘤

Abstract: 本文报道乳腺原发性恶性周围神经鞘膜瘤1例。患者女,18岁。主要临床表现为右侧乳房肿块,呈无痛进行性增大。超声表现为右侧乳房混合性巨大囊实性包块,边界尚清,可见少许血流;MRI表现为右侧乳房一巨大肿块,反转恢复序列脂肪抑制T 2WI呈不均匀高信号,内见低信号分隔影,T 1WI呈等低信号,边界清晰,DWI上肿瘤信号不均,以高信号为主,动态增强扫描示瘤体边缘及实性成分呈斑片状、结节状不均匀明显强化。病理诊断:右侧乳腺恶性周围神经鞘膜瘤。

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