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先天性眼外肌纤维化的MRI特征
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- Author:
- No author available
- Journal Title:
- Chinese Journal of Radiology
- Issue:
- 12
- DOI:
- 10.3760/cma.j.issn.1005-1201.2013.12.021
- Key Word:
- No keyword available
Abstract： 先天性眼外肌纤维化(congenital fibrosis of the extraocular m uscles,CFEOM)是一种遗传性非进展性疾病.病变特征为眼外肌广泛纤维化、眼球运动障碍、眼位偏斜,可伴有上睑下垂及全身其他系统的异常,发病率约为1/230 000[1].传统观点认为该病是原发性眼肌疾病,近年来的研究结果提示CFEOM可能是原发性神经病变继发肌源性改变的结果[2-3].笔者回顾性分析了6例散发CFEOM患儿的临床资料,以期发现CFEOM患者眼外肌及眼运动神经的MRI特征,为疾病的诊断和治疗提供影像依据.
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