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阴道斜隔综合征伴先天性尿道阴道瘘一例

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Author:
No author available
Journal Title:
Chinese Journal of Obstetrics and Gynecology
Issue:
10
DOI:
10.3760/cma.j.issn.0529-567x.2011.10.011
Key Word:
No keyword available

Abstract: 患者11岁,因月经初潮淋漓不尽伴持续性下腹痛13d入院.患者13 d前月经初潮,经量中,色鲜红,下腹持续性疼痛,尚能忍受,自行口服止痛药,未见好转.入院查体:一般情况可,痛苦面容,下腹压痛阳性,无反跳痛.肛诊:于左侧阴道旁触及-约6.0 cm ×4.0 cm ×4.0 cm囊性包块,张力较大,压痛可疑.妇科超声检查:盆腔内相当于子宫的位置见两个子宫回声,偏左侧者4.2 cm x3.0 cm,内膜厚0.6 cm,偏右侧者4.4 cm×3.0cm,内膜厚0.6 cm,宫壁回声欠均匀;阴道内见5.3 cm ×2.4 cm低回声,双侧卵巢未显示,双侧附件区未见明显包块.宫腔镜检查:未放置阴道窥器,进镜见阴道左侧壁近宫颈外口处向阴道内突出,经宫颈外口进入宫腔见内膜厚,有出血,可见一输卵管开口.结合超声检查考虑子宫畸形,双子宫,阴道斜隔,右侧子宫与右侧阴道相通,左侧子宫与左侧阴道斜隔内相通,血性液体积聚在左侧斜隔内形成包块.腹部彩超检查:左肾区及腹腔内未见明确的左肾回声.入院诊断:阴道斜隔综合征Ⅰ型,左肾缺如.在联合麻醉下行阴道斜隔切开术.于阴道斜隔膨隆最明显处穿刺,抽出暗红色黏稠液体,以穿刺针头为指示点,距处女膜缘2 cm处作纵行的上下小切口,可见大量暗红色血性液体流出,伸人手指能触摸到隔后腔隙及宫颈部位,触摸过程中可见少量暗红色血性液体白尿道外口溢出.请泌尿外科医师会诊,行膀胱镜检查,可见右侧输尿管开口,未见左侧输尿管开口,膀胱内见少量陈旧性暗红色血块,未见出血点,尿道未见出血点.排除术中尿道及膀胱损伤的可能.

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