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Cronkhite-Canada syndrome: A case report and review of the literature

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Author:
No author available
Journal Title:
World Chinese Journal of Digestology
Issue:
28
DOI:
10.11569/wcjd.v26.i28.1672
Key Word:
Cronkhite-Canada综合征;胃肠道息肉;外胚层改变;治疗

Abstract: Cronkhite-Canada综合征(Cronkhite-Canada's syndrome,CCS)是临床罕见病,病因及发病机制尚不明确,该病以胃肠道多发息肉及外胚层两大症候群为主,临床表现以腹泻为主,全消化道多发息肉,伴有皮肤色素沉着、毛发脱落、指(趾)甲萎缩脱落等.预后较差,本文报道1例CCS患者并对62篇国内文献进行回顾性分析.

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