Abstract: IntroductionNevus sebaceous (NS), also known as nevus sebaceous of Jadassohn, is a congenital sebaceous hyperplasia or organoid nevus. This benign congenital hamartoma is composed of abnormal epidermal and dermal com-ponents. The hamartomatous lesions, usually clinically present at birth, are most frequently distributed on areas with sebaceous glands, especially the scalp and face[1]. NS originates from pluripotent primordial epithelial germ tissue and occurs in approximately 0.1%of newborns.