Abstract: A case of infant malignant atrophic papulosis(also known as Degos' disease)is reported. The 8-month-old girl presented with recurrent erythematous papules with central porcelain-white depressions on the trunk and extremities. An erythematous papule was noticed on the abdomen by her mother 4 days after birth, which then became necrotic and umbilicated, healed rather slowly to leave a small white scar, surrounded by pink edematous border and telangiectases. Additional lesions developed in sequential fashion. A skin biopsy revealed mild edema in the upper dermis, with little mucin deposition and decreased adnexal structures. The overlying epidermis was atrophic. There was no apparent vasculopathy or perivascular infiltration of inflammatory cells. Considering only few active lesions, the patient was followed up closely without any treatment in the next 16 months. During this period, only a few small lesions developed, and no systemic symptom was present. Further follow-up is required to ascertain whether the diagnosis of the case is a benign cutaneous form of malignant atrophic papulosis.