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Nephrogenic Fibrosing Dermopathy

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Author:
No author available
Journal Title:
INTERNATIONAL JOURNAL OF DERMATOLOGY AND VENEREOLOGY
Issue:
1
DOI:
10.3760/cma.j.issn.1673-4173.2006.01.014
Key Word:
硬皮病局限性;纤维化;肾疾病

Abstract: 肾源性纤维化硬皮病是近年来新发现的一种皮肤病.该病和硬皮病的临床表现很相似,都是以局限性皮肤硬化为主要皮损表现.其组织病理特征:真皮层表达CD34的梭形细胞增殖并向下扩展到皮下脂肪组织,间质黏蛋白和弹性纤维轻度增加并伴弹性组织离解;胶原铁染色可见真皮浅层少量黏蛋白沉积.

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