Abstract： Objective To observe the echocardiographic diagnosis value of congenital dextrocardia and cardiovascular anomaly. Methods Seven-six patients with dextrocardia were classified according to Van Praagh's method. The cardiovascular anomalies were diagnosed by eehocardiography combined with operation results. Results Fourty-seven cases were mirror-image dextrecardia. 57.4 % of the 47 cases had concordant segmental connection, mostly with simple anomalies, including ASD and VSD with PH. Other patients with disconcordant segnental cormec tion were complicated with complex anomalies, including DORV, TGA, SV +PS or PAA. 23 cases were dextroversion, mostly with disconcordant segmental connection and complex anomalies, including DORV, SV, C-TGA and TGA + PS. 2 cases were left isomerism and 4 were right isomerism and these 6 cases presented with complex anomalies. Compared with the operation results, echocardiography could accurately detect congenital dextrocardia and cardiovas-cular anomalies, but there is still limitation for diagnosis of some anomalies. Conclusion Echocardiography can be the first choice for diagnosis of congenital dextrocardia.