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Imaging diagnoses of four cases with congenital aortic-left ventricular tunnel

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Author:
No author available
Journal Title:
CHINESE JOURNAL OF RADIOLOGY
Issue:
7
DOI:
10.3760/j.issn:1005-1201.2004.07.005
Key Word:
心脏缺损,先天性;心血管造影术

Abstract: 目的探讨先天性主动脉-左心室通道的影像表现和诊断特征.方法4例病人,男3例,女1例;年龄4~30岁,经超声心动图和心血管造影确诊为先天性主动脉-左心室通道.结果升主动脉造影显示主动脉根部有异常的囊袋样突出管道进入左心室腔内.1例拒绝手术,3例手术治疗,术中见升主动脉扩张,主动脉根部有一管状膨出形成隧道,引流入左心室腔,2例合并有主动脉瓣关闭不全,同时行隧道修补和主动脉瓣替换术,治愈出院.结论先天性主动脉-左心室通道是极为罕见的先天性心血管畸形,需早期诊断,尽早手术治疗,能避免出现主动脉瓣关闭不全和心力衰竭.

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