Abstract: @@ Undifferentiated embryonal sarcoma of the liver (UESL) was first described by Stacker and Ishak in 1978. It is a rare tumor that most often presents in childhood between 6 to 10 years of age. The adult patients diagnosed with UESL often show nonspecific symptoms with normal laboratory results. Ultrasonography, CT, or MRI often reveals a cystic mass. Complete surgical resection plus pre- and/or post-operative systemic chemotherapy offers the possibility of a cure.