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The clinicopathologic study of castleman disease

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Author:
No author available
Journal Title:
JOURNAL OF LEUKEMIA & LYMPHOMA
Issue:
1
DOI:
10.3760/cma.j.issn.1009-9921.2005.01.004
Key Word:
Castleman病;病理活检;治疗

Abstract: 目的提高对Castleman病的诊断和治疗水平.方法报告6例Castleman病,进行分析并复习相关文献.结果男性4例,女性2例,年龄8岁~54岁.临床分型:局灶型2例,多中心型4例.病理学分型:透明血管型5例,浆细胞型1例.局灶型经手术或术后放疗均治愈.多中心型中3例经干扰素或化疗联合激素治疗后病情稳定,1例出现复发.结论该病诊断主要依靠病理学确定.手术、化疗、抗病毒治疗可控制其发展.

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